What is ​Heterotaxy Syndrome (Isomerism)?

Also known as: heterotaxy, situs ambiguous

Heterotaxy syndrome is a rare birth defect that involves the heart and other organs where a child is born with organs on the opposite side of the body from where they are commonly located. Having a heart on the right side of the chest instead of the left is just one of many situations that can occur. Other bodily organs can be impacted as well.

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Reviewed by: Jack Wolfsdorf, MD, FAAP

This page was last updated on: 1/29/2019 3:21:13 PM